Collaborative treatment of huge intrathoracic meningoceles associated with neurofibromatosis type 1: a case report

Journal of Cardiothoracic Surgery

Jae Taek Hong¹  Kyu Do Cho²  Yong Jin Chang²  Deog Gon Cho² 

[1] Department of Neurosurgery, St. Vincent’s Hospital, College of Medicine, The Catholic University of Korea, 93 Jungbu-daero, Paldal-Gu, Suwon 442-723, Gyenggi-Do, Republic of Korea;Department of Thoracic and Cardiovascular Surgery, St. Vincent’s Hospital, College of Medicine, The Catholic University of Korea, 93 Jungbu-daero, Paldal-Gu, Suwon 442-723, Gyenggi-Do, Republic of Korea

关键词: Mediastinal disease;    Thoracic meningocele;   

Others  :  1233437
DOI  :  10.1186/s13019-015-0374-y

 received in 2015-05-11, accepted in 2015-11-02,  发布年份 2015

【 摘 要 】

Background

An intrathoracic meningocele is a relatively rare disease, and it commonly accompanies neurofibromatosis type 1. Patients tend to have no symptom but if its size is too large and compresses a lung and neighboring organs, it needs shunt drainage or surgical resection.

Case Presentation

Herein, we present the case of a 52 year-old female patient with huge intrathoracic meningoceles associated with neurofibromatosis type 1, who has complained about chest discomfort and dyspnea at rest. As for a preliminary treatment, a neurosurgeon had performed a cystoperitoneal shunt, but the symptoms continued and the size of mass and the amount of pleural effusion did not change significantly. Therefore, the huge thoracic meningoceles were successfully treated through the thoracotomic approach in combination with lumbar puncture and cerebrospinal fluid drainage.

Conclusions

It is reported that double huge intrathoracic meningoceles associated with neurofibromatosis type 1 was successfully treated by a shunting procedure followed by thoracotomic resection with collaboration of a neurosurgeon.

【 授权许可】

   
2015 Cho et al.

【 图 表 】

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