Giant plexiform neurofibroma with hemorrhage in cranio-maxillofacial region as depicted on CT and MRI

European Journal of Medical Research

W Deng¹  Q Wang¹  T Chen¹  Z Yang¹  Y Feng¹ 

[1] Department of Radiology, West China Hospital of Sichuan University, Chengdu, Sichuan, China

关键词: MR;    CT;    Hemorrhage;    Plexiform neurofibroma;   

Others  :  1093328
DOI  :  10.1186/2047-783X-15-2-84

 received in 2009-09-09, accepted in 2010-01-05,  发布年份 2010

【 摘 要 】

Plexiform neurofibroma (PN) is a rare benign tumor and a special subtype of neurofibromatosis type 1 (NF1). Though the incidence is low, giant PN of the craniomaxillofacial region could result in severe hemifacial hypertrophy which is known as a typical manifestation of NF1 in young children. Here, we retrospectively reported a giant plexiform neurofibroma with hemorrhage in the cranio-maxillofacial region detected by CT and MRI. In addition, a brief review of the relevant literature is presented.

【 授权许可】

   
2010 I. Holzapfel Publishers

【 图 表 】

Figure 1.

Figure 2.

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