Jejunoduodenal intussusception caused by a solitary polyp in a woman with Peutz-Jeghers syndrome: a case report

Journal of Medical Case Reports

Tuncay Yilmazlar¹  Ersin Ozturk¹  Pinar Sarkut¹  Ali Ozer¹ 

[1] Department of General Surgery, Uludag University Faculty of Medicine, Görükle 16059, Bursa, Turkey

关键词: Peutz-Jeghers syndrome;    Intussusception;    Duodenum;   

Others  :  822936
DOI  :  10.1186/1752-1947-8-13

 received in 2013-05-13, accepted in 2013-10-11,  发布年份 2014

【 摘 要 】

Introduction

Peutz-Jeghers syndrome is a rare autosomal dominant disorder characterized by hamartomatous polyps and characteristic mucocutaneous pigmentation. The hamartomatous polyps of Peutz-Jeghers syndrome can cause intestinal occlusion, especially in the small intestine. Intussusception is seen frequently in children, but rarely in adults.

Case presentation

We present the case of a 21-year-old female patient who was admitted to our emergency service with symptoms of ileus as a result of intussusception due to duodenal polyps. Radiological and endoscopic findings determined a jejunoduedonal intussusception. After an unsuccessful endoscopic attempt, a laparotomy was performed that revealed a polypoid mass originating from the fourth part of her duodenum, with intussusception of her proximal jejunum.

Conclusion

Intussusception caused by Peutz-Jeghers syndrome is a rare diagnosis and is mostly jejunojejunal or jejunoileal. Despite the fact that a few duodenojejunal cases have been reported, this is to the best of our knowledge the first case of jejunoduedonal intussusception in a patient with Peutz-Jeghers syndrome to be described in the literature.

【 授权许可】

   
2014 Ozer et al.; licensee BioMed Central Ltd.

【 图 表 】

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