Unusual findings in secondary hypertension: double orifice mitral associated to aortic coarctation, bicuspid aortic valve, and ventricular septal defect

International Archives of Medicine

Mohamed Cherti¹  Rachida Amri¹  Najat Mouine¹ 

[1] Department of Cardiology B, IBN SINA Hospital, Mohamed V University Souissi, Rabat, Morocco

关键词: Ventricular septal defect;    Double orifice mitral;    Bicuspid aortic valve;    Aortic coarctation;    Secondary hypertension;   

Others  :  802522
DOI  :  10.1186/1755-7682-7-14

 received in 2013-12-01, accepted in 2014-03-22,  发布年份 2014

【 摘 要 】

Double orifice mitral valve is a rare congenital anomaly presenting as the division of the mitral orifice into two anatomically distinct orifices, it is most often associated with other congenital heart defects such as left-sided obstructive lesions, ventricular septal defects or aortic coarctation. We report the case of a 15 year’s old boy, admitted for arterial hypertension, auscultation revealed a rude aortic systolic murmur. Femoral pulses were weak. Owing to the suspicion of aortic coarctation, transthoracic echocardiography was performed, the aortic coarctation with dilation of the aorta proximal to the stenosis was confirmed and bicuspid aortic valve was found with good function. The mitral valve was dysmorphic, having two orifices; it was divided into 2 separate valve orifices by a fibrous bridge. No mitral or aortic regurgitation was documented by color Doppler flow imaging. The left ventricular ejection fraction was normal. There was a small peri membranous ventricular septal defect with left to right shunt. Owing to the severity of the aortic coarctation and taking into account the anatomy and characteristics of the patient, he was made a surgical correction of aortic coarctation with good outcome.

【 授权许可】

   
2014 Mouine et al.; licensee BioMed Central Ltd.

【 图 表 】

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