Congenital cholesteatoma of the infratemporal fossa with congenital aural atresia and mastoiditis: a case report

BMC Ear, Nose and Throat Disorders

Mosaad Abdel-Aziz¹ 

[1] Department of Otolaryngology, Faculty of Medicine, Cairo University, Cairo, Egypt

关键词: Infratemporal fossa;    Mastoiditis;    Congenital aural atresia;    Congenital cholesteatoma;   

Others  :  862800
DOI  :  10.1186/1472-6815-12-6

 received in 2011-09-02, accepted in 2012-06-13,  发布年份 2012

【 摘 要 】

Background

Congenital cholesteatoma may be expected in abnormally developed ear, it may cause bony erosion of the middle ear cleft and extend to the infratemporal fossa. We present the first case of congenital cholesteatoma of the infratemporal fossa in a patient with congenital aural atresia that has been complicated with acute mastoiditis.

Case presentation

A sixteen year old Egyptian male patient presented with congenital cholesteatoma of the infratemporal fossa with congenital aural atresia complicated with acute mastoiditis. Two weeks earlier, the patient suffered pain necessitating hospital admission, magnetic resonance imaging revealed a soft tissue mass in the right infratemporal fossa. On presentation to our institute, Computerized tomography was done as a routine, it proved the diagnosis of mastoiditis, pure tone audiometry showed an air-bone gap of 60 dB. Cortical mastoidectomy was done for treatment of mastoiditis, removal of congenital cholesteatoma was carried out with reconstruction of external auditory canal. Follow-up of the patient for 2 years and 3 months showed a patent, infection free external auditory canal with an air-bone gap has been reduced to 35db. One year after the operation; MRI was done and it showed no residual or recurrent cholesteatoma.

Conclusions

Congenital cholesteatoma of the infratemporal fossa in cases of congenital aural atresia can be managed safely even if it was associated with mastoiditis. It is an original case report of interest to the speciality of otolaryngology.

【 授权许可】

   
2012 Abdel-Aziz et al.; licensee BioMed Central Ltd.

【 图 表 】

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