Spinal intradural metastasis from scapular Ewing sarcoma

BMC Research Notes

Kulatunga Wijekoon Mudiyanselage Pramitha Prabhashini Kumarihamy²  Ekanayake Mudiyanselage Madhushanka Ekanayake¹  Kushalee Poornima Jayawickreme¹  Dissanayake Mudiyanselage Priyantha Udaya Kumara Ralapanawa¹ 

[1] Department of Medicine, University of Peradeniya, Peradeniya, Sri Lanka;University Medical Unit, Teaching Hospital Peradeniya, Peradeniya, Sri Lanka

关键词: Sri Lanka;    Spinal metastasis;    Scapular bone neoplasm;    Flaccid paralysis;    Ewing sarcoma;   

Others  :  1231576
DOI  :  10.1186/s13104-015-1263-0

 received in 2015-05-14, accepted in 2015-06-30,  发布年份 2015

【 摘 要 】

Background

Ewing sarcoma is a primary bone neoplasm, which is a high grade aggressive small round blue cell tumour, and is currently recognized as a part of the Ewing family of tumours. It is the most lethal bone tumor, and is a rare malignant bone tumor accounting for 10% of all primary bone tumors, and 6% of malignant bone tumors. It has an average annual incidence of 3 per 1 million, found almost exclusively in Caucasians. It commonly occurs in long bones and pelvis but rarely involves the scapula. 85% of cases have metastasis within 2 years of diagnosis, rarely involving the meninges.

Case presentation

We report a case of a 25 year old Sinhalese Sri Lankan female, presenting with a 1 day history of bilateral lower limb weakness and urinary incontinence. She had a sensory level with flaccid paralysis of lower limbs and a painless bony lump in the left dorsal scapula. Investigations showed scapular primary Ewing sarcoma giving rise to spinal intradural metastasis. For the best of our knowledge this is the first reported case of a scapular Ewing sarcoma with spinal intradural metastasis presenting with lower limb paralysis.

Conclusion

Intradural spinal metastasis of Ewing sarcoma presenting with lower limb weakness, without a history of pain, though rarely, can be the first presentation, and can rapidly progress to brainstem involvement and death.

【 授权许可】

   
2015 Ralapanawa et al.

【 图 表 】

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