Resection of a malignant paraganglioma located behind the retrohepatic segment of the inferior vena cava

BMC Surgery

Yang Zhao¹  Yongqing Xu¹  Feng Xu¹  Songlin Peng¹  Xianmin Bu¹  Chaoliu Dai¹  Xinlu Wang²  Changjun Jia¹ 

[1] Department of General Surgery, China Medical University, 110004 Shenyang, Liaoning Province, P.R. China;Department of Ultrasound Medicine, Shengjing Hospital, China Medical University, 110004 Shenyang, Liaoning Province, P.R. China

关键词: Malignant;    Partial hepatectomy;    Inferior vena cava;    Paraganglioma;   

Others  :  1123307
DOI  :  10.1186/1471-2482-13-49

 received in 2012-12-26, accepted in 2013-10-23,  发布年份 2013

【 摘 要 】

Background

Resection of a retrocaval paraganglioma is technically challenging due to limited tumor accessibility and proximity to the vena cava.

Case presentation

A large, malignant paraganglioma was found behind the retrohepatic segment of the inferior vena cava of a 60-year-old male. During resection of this rare paraganglioma, the left lateral lobe of the liver, a portion of the caudate lobe of the liver, and the gallbladder were also removed. Unfortunately, the patient died six months after surgery due to hepatic metastasis.

Conclusion

This case demonstrates that a partial hepatectomy may be necessary to improve tumor accessibility during resection of a retrocaval paraganglioma, particularly if the tumor is proximal to the vena cava. Furthermore, palliative treatments may help prevent tumor recurrence and metastasis of malignant paragangliomas.

【 授权许可】

   
2013 Jia et al.; licensee BioMed Central Ltd.

【 图 表 】

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