Common bile duct adenocarcinoma in a patient with situs inversus totalis: report of a rare case

BMC Research Notes

Arnaud Roth³  Omar El Mesbahi⁴  Muriel Genevay⁵  Thai Nguyen-Tang⁶  Thierry Berney¹  Sylvain Terraz²  Saoussane Kharmoum⁴  Hafida Benhammane⁴ 

[1] Department of general surgery, University Hospitals of Geneva, Geneva, Switzerland;Department of radiology, University Hospitals of Geneva, Geneva, Switzerland;Department of medical oncology, University Hospitals of Geneva, Geneva, Switzerland;Department of medical oncology, Hassan II University Hospital, Fez, Morocco;Department of pathology, University Hospitals of Geneva, Geneva, Switzerland;Department of gastroenterology, University Hospitals of Geneva, Geneva, Switzerland

关键词: Surgical management;    Preoperative staging;    Bile duct cancer;    Situs inversus totalis;   

Others  :  1165033
DOI  :  10.1186/1756-0500-5-681

 received in 2012-09-30, accepted in 2012-11-27,  发布年份 2012

【 摘 要 】

Background

Situs inversus totalis represents an unusual anomaly characterized by a mirror-image transposition of the abdominal and thoracic viscera. It often occurs concomitantly with other disorders that make difficult diagnosis and management of abdominal pathology. The relationship between situs inversus totalis and cancer remains unclear.

Case presentation

We describe a 33-year old Guinean man with situs inversus totalis who presented with obstructive jaundice. Imaging and endoscopic modalities demonstrated a mass of distal common bile duct which biopsy identified an adenocarcinoma. The patient was successfully treated by cephalic pancreaticoduodenectomy followed by adjuvant chemoradiation and he is doing well without recurrence 8 months after surgery.

Conclusion

The occurrence of bile duct adenocarcinoma in patient with situs inversus totalis accounts as a rare coincidence. In this setting, when the tumor is resectable, surgical management should be considered without contraindication and must be preceded by a careful preoperative staging.

【 授权许可】

   
2012 Benhammane et al.; licensee BioMed Central Ltd.

【 图 表 】

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