Scleredema-an uncommon cause of swelling in a child-a case report and review of the literature

BMC Research Notes

Rajesh Panth²  Arun Kumar Neopane¹  Bikash Shrestha¹ 

[1] Department of Paediatrics, Nepalese Army Institute of Health Sciences, Shree Birendra Hospital, Swayambhu, Chhauni, Kathmandu, Nepal;Department of Pathology, Nepalese Army Institute of Health Sciences, Shree Birendra Hospital, Swayambhu, Chhauni, Kathmandu, Nepal

关键词: Systemic sclerosis;    Scleromyxedema;    Scleroderma;    Buschke;   

Others  :  1130159
DOI  :  10.1186/1756-0500-7-571

 received in 2014-08-13, accepted in 2014-08-22,  发布年份 2014

【 摘 要 】

Background

Body swelling in a child is a common symptom. Apart from systemic causes like renal, hepatic, and cardiac, rarely such a swelling may be caused by dermatologic conditions.

Case presentation

A child presented with swelling of the body which was subsequently diagnosed as scleredema, a rare and benign dermatologic condition. Scleredema can be confused with similar sounding terms like scleroderma and scleromyxedema.

Conclusions

The case is presented to highlight scleredema as a rare cause of body swelling in paediatrics and to differentiate it from similar sounding rare terms like scleroderma and scleromyxedema.

【 授权许可】

   
2014 Shrestha et al.; licensee BioMed Central Ltd.

【 图 表 】

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【 参考文献 】

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