Retinoblastoma in an adult

BMC Research Notes

Nadeem Zafar¹  Saqib Qayyum Ahmad³  Saemah Nuzhat Zafar² 

[1] Armed Forces Hospital, Najran, Kingdom of Saudi Arabia;Department of Pediatric Ophthalmology and Strabismus, Al-Shifa Trust Eye Hospital, Rawalpindi 46000, Pakistan;Department of Pathology, PAF Hospital, Islamabad, Pakistan

关键词: Optic nerve;    Cytology;    Histopathology;    Eye enucleation;    CT-Scan;    Ultrasonography;    Glaucoma;    Neovascular;    Retinoblastoma;   

Others  :  1142006
DOI  :  10.1186/1756-0500-6-304

 received in 2012-08-24, accepted in 2013-07-30,  发布年份 2013

【 摘 要 】

Background

Retinoblastoma is the most common pediatric ocular tumour. It may rarely present in adults. The present case adds to the number of 26 cases already published in literature since 1919 till 2013. Our aim is to highlight the rare occurrence of retinoblastoma in adults along with its features which differentiate it from paediatric retinoblastoma.

Case presentation

We describe a case of adult onset retinoblastoma (group E, according to the international classification of retinoblastoma) occurring in a 25 year old male. He presented with decreasing visual acuity in the right eye of 4 months duration. He had neo-vascular glaucoma and pseudohypopyon. B scan ultrsonography of his right eye showed intraocular growth without any calcification. The CT scan of the orbits and brain showed intraocular growth in the right eye with no calcification. Enucleation of the right eye was carried out. Retinoblastoma was confirmed on histopathology of the enuleated globe.

Conclusions

The present case adds to the number of adult Rb patients reported in literature. Early detection to salvage the life can be made possible if the clinician keeps a high index of suspicion when observing retinal mass of adult onset. Proper counselling of the patient in order to seek his full involvement in management may help in improving the prognosis of the disease.

【 授权许可】

   
2013 Zafar et al.; licensee BioMed Central Ltd.

【 图 表 】

Figure 1.

Figure 2.

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